Research Interests:
Dr. Driscoll, as part of a SCOR in Pediatric Cardiovascular
Disease, is studying the genetic basis of non-syndromic
conotruncal cardiac malformations. The laboratory has
established a bank of DNA and cell lines from individuals
with congenital cardiac defects which will serve as the
basis for future studies on the genetics of congenital
heart disease.
Dr. Driscoll's previous research focused on understanding
the genetic basis of two genetic disorders, DiGeorge
syndrome and velocardiofacial sydrome. Using molecular and
cytogenetic techniques her laboratory has shown that the
vast majority of patients with these disorders have
microdeletions of chromosome 22q11. Dr. Driscoll's initial
studies defined a critical region within chromosome 22
responsible for these disorders and the laboratory is
currently utilizing translocation breakpoint mapping to
further refine this region and narrow our search for the
genes responsible for the phenotypic features observed in
these patients. As a result of this research Dr. Driscoll
and her colleagues at Children's Hospital have developed a
diagnostic assay for the detection of deletions utilizing
fluorescence in situ hybridization. Currently, Dr. Driscoll
is examining modifying genes which may influence phenotypic
variability.
Recent Representative Publications:
Stalmans I, Lambrechts D, De Smet F, Janssen S, Wang J,
Maity S, Kneer P, von der Ohe M, Swillen A, Maes C,
Gewillig M, Molin DGM, Hellings P, Boetel T, Haardt M,
Compernolle V, Dewerchin M, Plaisance S, Vlietinck R,
Emanuel B, Gittenberger-de Groot AC, Esguerra CV, Scambler
P, Morrow B, Driscoll DA, Moons L, Carmeliet G, Behn-Krappa
A, Devriendt K, Collen D, Conway SJ, Carmeliet P: VEGF: A
modifier of the del22q11 (DiGeorge) syndrome? Nature
Medicine 9(2):1-10, 2003.
Saitta, S.C., Harris, S.E., McDonald-McGinn, D.M., Emanuel,
B.S., Tonnesen, M.K., Zackai, E.H., Seitz, S.C., Driscoll,
D.A.: Independent de novo 22q11.2 deletions in first
cousins with DiGeorge/velocardiofacial syndrome. Am. J.
Med. Genet. 124A:313-317, 2004.
Seeber, B., Driscoll, D.A.: Hereditary breast and ovarian
cancer syndrome: should we test adolescents? J. Pediatr.
Adolesc. Gynecol. 124A:213-7, 2004.
Morgan MA, Driscoll DA, Mennuti MT, Schulkin J: Practice
patterns of obstetrician-gynecologists regarding
preconception and prenatal screening for cystic fibrosis.
Genetics in Medicine 6(5): 450-55, 2004.
Watson MS, Cutting GR, Desnick RJ, Driscoll DA, Klinger K,
Mennuti MT, Palomaki GE, Popovich BW, Pratt VM, Rohlfs EM,
Strom CM, Richards CS, Witt DR, Grody WW: Cystic Fibrosis
(CF) population carrier screening: 2004 revision of ACMGs
mutation panel. Genetics in Medicine 6:387-91, 2004.
Merrill A., Rosenblum-Vos, L., Driscoll, D.A., Daley K.,
Treat K.: Prenatal diagnosis of Fanconi Anemia (group c)
subsequent to abnormal sonographic findings. Pren Diag 25::
20-22, 2005.
Lambrechts, D., Deviendt, K., Driscoll, D.A., Goldmuntz,
E., Gewillig, M., Vlietinck, R., Collen, D., Carmeliet, P.:
Low expression VEGF haplotype increases the risk for
tetralogy of Fallot: a family-based association study. J.
Med. Genet. 42:519-522, 2005.
Sherman, S., Pletcher, B.A., Driscoll, D.A.: Fragile X
Syndrome: Diagnostic and carrier testing Genet. Med..
7:584-7, 2005.
Driscoll, D.A., Boland, T.. Emanuel, B.S., Kirschner, R.K.,
Larossa, D., Manson, J., et. al.: Evaluation of potential
modifyers of the palatal phenotype in the 22q11.2 deletion
syndrome. Cleft Palate Craniofac. J. 43:435-441, 2006.
Driscoll, D.A.: Molecular and genetic aspects of
DiGeorge/velocardiofacial syndrome. Methods Mol. Med.
126:43-55, 2006.
Pletcher, B. A., Toriello, H. V., Noblin, S. J., Seaver, L.
H., Driscoll, D. A., Bennett, R. L., and Gross, S. J.:
Indications for genetic referral: a guide for healthcare
providers. Genet Med 9, 385-389, 2007.
